Frontiers Lysosomal and Mitochondrial Liaisons in Niemann-Pick

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Niemann-Pick type C2 deficiency impairs autophagy-lysosomal activity, mitochondrial function, and TLR signaling in adipocytes - ScienceDirect

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

PDF) Quantitative imaging of membrane contact sites for sterol transfer between endo-lysosomes and mitochondria in living cells

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

Correction of Niemann-Pick type C1 disease with the histone deacetylase inhibitor valproic acid

The NPC1ASO mouse model shows physiological and pathological liver

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

Figures and data in Lysosomal cholesterol export reconstituted from fragments of Niemann-Pick C1

Loss of NPC1 enhances phagocytic uptake and impairs lipid trafficking in microglia

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

A proposed model for the pathogenesis of Niemann-Pick disease type

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